Skip to main content

Part of Cancer staging guidance sheets

Rhabdomyosarcoma and other soft tissue sarcomas (CTYA)

Previous Chapter

Non-hodgkin lymphoma (children)

Current Chapter

Current chapter – Rhabdomyosarcoma and other soft tissue sarcomas (CTYA)

View all

Next Chapter

Wilms tumour of the kidney

Page contents

Introduction

This is the data sheet for UICC TNM 8th edition staging of rhabdomyosarcoma and other soft tissue sarcomas (CTYA).

For more detailed information regarding TNM staging, please see pages 248-249 of the UICC TNM 8 book or visit the Wiley and UICC website.

Stage groupings

Stage Group

T stage

N stage

M stage

 Anatomic sites

Stage I

Any T

Any N

M0

 Favourable site

Stage II

T1a, T2a

N0

M0

 Unfavourable site

Stage III

T1a, T2a

N1

M0

 Unfavourable site

T1b, T2b

Any N

M0

 Unfavourable site

Stage IV

Any T

Any N

M1

 Any site

 

IRS group Classification

I

- Localised disease, completely resected (regional nodes not involved) - Confined to muscle or organ of origin

- Contiguous involvement with infiltration outside the muscle or organ of origin, as through fascial planes

II

- Grossly resected tumour with microscopic residual disease

- No evidence of gross residual tumour; no evidence of regional node involvement

- Regional disease, completely resected (regional nodes involved and/or extension of tumour into an adjacent organ); all tumour completely resected with no microscopic residual tumour

- Regional disease with involved nodes, grossly resected, but with evidence of microscopic residual

III

- Incomplete resection or biopsy with gross residual disease

IV

- Distant metastatic disease present at onset (lung, liver, bones, bone marrow, brain, and distant muscle and nodes)

Favourable anatomic sites: Orbit, head and neck(excluding parameningeal tumours) and genitourinary sites (excluding bladder and prostate tumours.

Unfavourable anatomic sites: Bladder, prostate, extremity, cranial, parameningeal, trunk, retroperitoneum and all other sites not noted as favourable.

TNM clinical classification

T - primary tumour

T value Description

TX

Primary tumour cannot be assessed

T0

No evidence of primary tumour

T1

Confined to a single anatomic site

T1a

Tumour 5 cm or less in greatest dimension

T1b

Tumour more than 5 cm in greatest dimension

T2

Extension beyond anatomic site

T2a

Tumour 5 cm or less in greatest dimension

T2b

Tumour involves more than half of one lobe, but not both lobes

N - regional lymph nodes

N value Description

NX

Regional lymph nodes cannot be assessed

N0

No regional lymph node metastasis

N1

Regional lymph node metastasis

M - distant metastasis

M value Description

M0

No distant metastasis

M1

Distant metastasis

Download

Click on the box below to download a PDF version of this data sheet:

Last edited: 29 December 2022 3:22 pm

Previous Chapter

Non-hodgkin lymphoma (children)

Next Chapter

Wilms tumour of the kidney
  1. Cancer staging guidance sheets
  2. Lip and oral cavity (ICD10 C00, C02-C06)
  3. Malignant melanoma of upper aerodigestive tract (ICD10 C00-06, C10-14, C30-32)
  4. Pharynx (ICD10 C01, C05.1-2, C09, C10.0, C10.2-3, C11-13)
  5. Major salivary glands (ICD10 C07, C08)
  6. Oesophagus including oesophagastric junction (ICD10 C15 & C16.0)
  7. Stomach (ICD10 C16 except C16.0)
  8. Small intestine (ICD10 C17)
  9. Appendix (ICD10 C18.1)
  10. Colon and rectum (ICD10 C18-C20)
  11. Anal canal and perianal skin data (ICD10 C21, C44.5)
  12. Liver (ICD10 C22.0)
  13. Intrahepatic bile ducts (ICD10 C22.1)
  14. Gallbladder (ICD10 C23, C24.0)
  15. Distal extrahepatic bile duct (ICD10 C24.0)
  16. Perihilar bile ducts (ICD10 C24.0)
  17. Ampulla of vater (ICD10 C24.1)
  18. Pancreas (ICD10 C25)
  19. Nasal cavity and paranasal sinuses (ICD10 C30.0, C31.0, C31.1)
  20. Larynx (ICD10 C32.0 C32.1, C32.2, C10.1)
  21. Lung (ICD10 C34)
  22. Thymic tumours (ICD10 C37)
  23. Soft tissues (ICD10 C38.1-2, C47-C49)
  24. Bone (ICD10 C40 & C41)
  25. Malignant melanoma of skin (ICD10 C43, C51.0, C60.9, C63.2)
  26. Merkel cell carcinoma of skin (ICD10 C44 & C63.2)
  27. Skin carcinoma of the head and neck (ICD10 C44.0, C44.2-4)
  28. Carcinoma of skin of the eyelid (ICD10 C44.1)
  29. Carcinoma of skin (excluding eyelid, head and neck, perianal, vulva and penis) (ICD10 C44.5-7, C63.2)
  30. Pleural mesothelioma (ICD10 C45)
  31. Breast tumours (ICD10 C50)
  32. Vulva (ICD10 C51)
  33. Cervix uteri (ICD10 C53)
  34. Uterine sarcomas
  35. Uterus - endometrium (ICD10 C54.1, C55)
  36. Ovarian, fallopian tube and primary peritoneal carcinoma (ICD10 C56, C57, C48.1, C48.2)
  37. Gestational trophoblastic neoplasms (ICD10 C58)
  38. Penis tumours (ICD10 C60)
  39. Prostate tumours (ICD10 C61)
  40. Testis tumours (ICD10 C62)
  41. Kidney tumours (ICD10 C64)
  42. Renal pelvis and ureter tumours (ICD10 C65 & C66)
  43. Urinary bladder tumours (ICD10 C67)
  44. Urethra tumours (ICD10 C68.0)
  45. Carcinoma of conjuctiva (ICD10 C69.0)
  46. Malignant melanoma of conjuctiva (ICD10 C69.0)
  47. Retinoblastoma (ICD10 C69.2)
  48. Malignant melanoma of uvea (ICD10 C69.3, C69.4)
  49. Carcinoma of lacrimal gland (ICD10 C69.5)
  50. Sarcoma of orbit (ICD10 C69.6)
  51. Thyroid gland (ICD10 C73)
  52. Adrenal cortex (ICD10 C74.0)
  53. Chronic lymphocytic leukaemia
  54. Hepatoblastoma (CTYA)
  55. Hodgkins and non-hodgkins lymphoma (ICD10 C81-88)
  56. Medulloblastoma
  57. Multiple myeloma
  58. Neuroblastoma
  59. Neuroendocrine tumours of the foregut
  60. Neuroendocrine tumours of the midgut and hindgut
  61. Non-hodgkin lymphoma (children)
  62. Rhabdomyosarcoma and other soft tissue sarcomas (CTYA)
  63. Wilms tumour of the kidney